Shortlasting unilateral neuralgiform headache attacks. If the address matches an existing account you will receive an email with instructions to retrieve your username. Shortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearing sunct syndrome is a rare headache. This study was designed to evaluate the efficacy of gabapentin gbp in the treatment of shortlasting unilateral neuralgiform headache with conjunctival injection and tearing sunct syndrome on a relatively large sample of persian patients. Sunct syndrome, sunct headache, shortlasting unilateral neuralgiform headache attacks with conjunctival injection or tearing, suna headache, shortlasting unilateral neuralgiform headache attacks with cranial autonomic symptoms. Frontiers comorbid sunct syndrome and opalski syndrome. Sunct syndrome is an acronym for shortlasting unilateral neuralgiform headache with conjunctival injection and tearing, it is a type of painful headache that is characterized as one sided and usually around the eye area. Despite a myriad of therapeutic trials, no convincingly effective remedy for sunct and suna is available at present. After treatment onset, he experienced intense and pulsatile headache episodes. It is characterized by shortlasting unilateral attacks of severe neuralgiform pain associated. A set of diagnostic criteria of sunct syndrome is also given. Report of a case and treatment update cosme gayescoda 1, gemma mayorsubirana 2, octavi campsfont 3, leonardo beriniaytes 4 1 md, dds, ms, phd. This article includes discussion of sunct, shortlasting unilateral neuralgiform. This means that sunct syndrome, or a subtype of sunct syndrome, affects less than 200,000 people in the us population.
The pain is maximal in and around the eye and may radiate to the ipsilateral forehead, temple, nose, cheek, and palate 4. It usually involves the ophthalmic division of the trigeminal nerve but, rarely, it may involve any part of the head. Symptoms include excruciating burning, stabbing, or electrical headaches mainly near the eye. All papers published in english or german were considered when they described a controlled trial or a case series on the treatment of at least. Sunct syndrome and seborrheic dermatitis associated with craneosynostosis. Shortlasting unilateral neuralgiform headache attacks with. S hortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing syndrome is a rare headache disorder classified under tac. Medical treatment options include lamotrigine, topiramate. Shortlasting unilateral neuralgiform headache with conjunctival injection and tearing syndrome is a rare condition hardly ever encountered by those dealing with pain and may be confused with other pain types with autonomic origin. The pain is described as throbbing, sharp or stabbing. Hemicrania continua hc, paroxysmal hemicrania ph and short lasting neuralgiform headache attacks sunct and suna are rare syndromes with a difficult therapeutic approach.
Diagnosis and treatment of this condition are challenging. Trauma, arteriovenous malformations and pituitary adenomas may have a causative role. Paroxysmal hemicrania often the result of cervical pressure sunct syndrome, sjaastad syndrome, ion, on, gpn, etc. Shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct is a primary headache syndrome. Sunct syndrome treated with gamma knife targeting the. Genetic and rare diseases information center gard po box 8126, gaithersburg, md 208988126 tollfree. The guild welcomes all editors with a good grasp of english and wikipedia s policies and guidelines to help in the drive to improve articles. If you do not see its contents the file may be temporarily unavailable at the journal website or you do not have a pdf plugin installed and enabled in your browser. The syndrome has been described more fully over subsequent years sjaastad et al. The intense pain is typically localized at the distribution of the first division. Sunct syndrome successfully treated with the combination of oxcarbazepine and gabapentin sunct syndrome successfully treated with the combination of oxcarbazepine and gabapentin marziniak, martin. Red ear syndrome precipitated by a dietary trigger. Sunct syndrome successfully treated with the combination.
A version of this article was copy edited by despayre, a member of the guild of copy editors, on march 4, 2012. Visit our project page if youre interested in joining. Sunct headache is a clinical diagnosis supported by a combination of clinical history, normal physical examination, radiography, and mri. The patient was followed under lamotrigine treatment for 6 months and was symptom free during that period. Symptoms are brought on by touch, exertion, heat or cold, stress, neck movements and washing or brushing of hair. Sunct syndrome is one of a number of trigeminal autonomic cephalalgias characterized by shortlasting headache occurring in the first division of the trigeminal nerve 2,3.
Sunct syndrome has been previously described in association with lms. Chairman and professor of oral and maxillofacial surgery. The disorder is marked by bursts of moderate to severe burning, piercing, or throbbing pain, usually on one side of the head and around the eye or temple. If you have problems viewing pdf files, download the latest version of adobe reader. Matharu senior lecturer and honorary consultant neurologist, headache group, institute of neurology and the national hospital for neurology and neurosurgery, queen square, london, wc1n 3bg, uk 1 g. Case report sunct syndrome successfully treated with the. Opalski syndrome is a rare variation of lateral medullary syndrome lms accompanied by ipsilateral hemiparesis.
New on here and have complicated sunct im tony, im 35, i have been getting the headaches everyday for about a year, and the amount varies but averages about 20 a day. It can be distinguished from other closely similar primary headaches because of the usually very brief attack duration 15120 seconds which can. Sunct syndrome in two patients with prolactinomas and bromocriptineinduced attacks. Red ear syndrome is a rare condition characterized by episodic attacks of erythema of the ear accompanied by burning ear pain. Sunct syndrome risks, symptoms and leading causes treato. Sunct syndrome shortlasting unilateral neuralgiform. On a good day i might just have 34, but the worst ive had was more like 70 in a day. Shortlasting unilateral neuralgiform headache with conjunctival injection and tearing sunct is classified by the international headache society as a primary headache disorder. Pain syndromes that may mimic sunct headache include cluster headache, temporal arteritis, trigeminal neuralgia involving the first division of the trigeminal nerve, demyelinating disease, primary stabbing headache, hypnic headache, and chronic paroxysmal. The attacks are strictly unilateral, generally with the pain persistently confined to the ocularperiocular area. This case demonstrates the effectiveness of resection as definitive treatment for sunct syndrome associ ated with tumoral compression of the trigeminal nerve. Friends, employers, and colleagues cluster headache.
Suna shortlasting unilateral neuralgiform headache attacks with cranial autonomic symptoms. Since this initial description approximately 100 cases have been reported in the literature 25. Therefore, its differential diagnosis and treatment are challenging and disputable. Short lasting unilateral neuralgiform headache attacks with conjuntival injection and tearing sunct also manifests itself as a onesided headache and is associated with the autonomic symptoms as described in cluster headache ch. Patients report brief attacks of unilateral, stabbing and throbbing headache lasting between 5 and. Sunct syndrome treated with gamma knife targeting the trigeminal nerve and sphenopalatine ganglion, the journal of headache and pain, 2012, pp. The case we report here involves a woman whose symptoms were brought on by a dietary. Although rarely seen, clinical status may be a feature of the sunct syndrome. The reported sunct patient is the first who responded to a combination treatment of oxcarbazepine and gabapentin.
Lets not forget that there are 12 pairs of cranial nerves that feed in the pharengeal arches in some measure. Pareja and sjaastad, 1997, although only in small series. Primary res appears to have a frequent association with primary headaches especially migraine. Sunct syndrome is listed as a rare disease by the office of rare diseases ord of the national institutes of health nih. Shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct is a rare but disabling primary headache disorder characterized by brief, severe, ipsilateral, orbitotemporal pain with autonomic features such as conjunctival injection, tearing, and rhinorrhea. Sunct emerges as a fairly clearcut, clinical syndrome. The headache seemed rather stable at this level until he, at 58, was struck by the end of a fishing rod in the lower, medial, supraorbital area on the symptomatic side. The present report describes a sunct syndrome in a 64yearold male who had been diagnosed with trigeminal neuralgia several years ago. Shortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearing sunct syndrome and tumor of. Sunct headache information page national institute of.
Eight patients with sunct syndrome underwent a 4week, openlabel, daily treatment with 600900 mg gbp. If you have questions, please direct them to our talk page. Although intravenous lidocaine can be used as a transitional treatment until beneficial effects of a preventive treatment becomes evident. The patient reported stabbing pain in the orbital zone and in the left upper maxillary region, of great intensity, brief duration, and a frequency of 20100 attacks a day. Clinical description the disease manifests with strictly unilateral pain attacks of moderatetosevere intensity. The cause of sunct is unknown, but some think it involves a disturbance in a particular part of the brain, which may also involve the trigeminal nerve. Red ear syndrome res is characterised by attacks of unilateral or bilateral burning ear pain associated with erythema. Here, we describe the case of a woman with shortlasting unilateral neuralgiform attacks with cranial autonomic symptoms suna. Sunct, pathophysiology, treatment, and trial last search in january, 2005. Pathogenesis, surgical treatment, and cure for sunct syndrome. I cant remember that my boss was a trigger for sunct attacks. A few cases of sunct syndrome have been reported in children. Introduction shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct is a rare primary headache syndrome first described in 1978 sjaastad et al.
At around 30, this male patient had developed cycles of unilateral, ocularperiorbital, mostly lowgrade pain sjaastad et al 1978. In sunct, pain paroxysms are typically periorbital, are extremely frequent up. This page includes the following topics and synonyms. Sunct, like cluster headache, is a primary headache disorder characterized by unilateral pain in the trigeminal nerve distribution and by autonomic manifestations. Headache in sunct universitair pijn centrum maastricht. Sunct shortlasting unilateral neuralgiform headache attack with. As such, sunct and cluster headaches are sometimes grouped together as trigeminal autonomic cephalgias. Efficacy of gabapentin in the treatment of sunct syndrome. The patient reported stabbing pain in the orbital zone and in the left upper maxillary region, of great intensity, brief duration, and a. Sunct shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing.
Results for sunct syndrome 1 8 of 8 sorted by relevance date click export csv or ris to download the entire page or use the checkboxes to select a subset of records to download export csv export ris 10 per page 50 per page 100 per page 250 per page. Shortlasting unilateral neuralgiform headaches with conjunctival injection and tearing sunct is a rare headache syndrome which belongs to the trigeminal autonomic cephalalgias. Shortlasting unilateral neuralgiform headache mafiadoc. Sunct headache genetic and rare diseases information. Sunct syndrome successfully treated with topiramate. Suna, sunct, red ear syndrome, trigeminal autonomic cephalalgias, cranial autonomic symptoms background red ear syndrome res is a rare condition originally described by lance 1. We describe one case of sunct syndrome secondary to consumption of. Indeed, an observation period of more than 5 years speaks against a symptomatic etiology of sunct in these cases. The first sunct patient was observed in 1977, at 62 years of age. Sunct syndrome in association with persistent horner syndrome in a chinese patient. Sunct shortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearingis a rare form of headache that is most common in men after age 50.
261 790 314 455 1302 227 349 672 1048 1477 1428 1073 214 1430 281 241 38 1206 1128 778 666 1181 1360 1285 264 366 981 1012 633 973